Congenital cholesteatoma: a review

Congenital cholesteatoma (CC) is a whitish mass lesion found in the middle ear cleft behind intact tympanic membrane early life. It relatively uncommon disease and shows its growth extension over period of time. CC evidenced with no prior history perforation, otorrhea, previous otologic procedures, normal pars tensa, flaccida. The etiopathogenesis still controversial; however, epithelial cell rest theory most commonly accepted one. common sites are anterior-superior posterior-superior quadrants cavity. clinical presentation conductive hearing loss. Early detection intervention needed to avoid complications CC. treatment choice surgical. frequency recurrence seems be lower patients than acquired cholesteatoma. Rapid progression may occur older children has been associated advanced There very few reports for available medical literature This objective this review article discuss prevalence, etiopathology, manifestations, diagnosis, treatment.